Answer:
Lysosomes
Explanation:
Tay-sachs disease is a rare Autosomal recessive disease that causes neurodegenerative disorder.
Deficiency of an enzyme Hexosaminidase A results in excessive accumulation of gangliosides (sialic acid containing glycosphingolipids) in the brain and nerve cells.
It is a lysosomal storage disease .Absence of the enzyme Hexosaminidase A ,that breakdowns substance like fats results in accumulation of such substance in the lysosomes.Too much accumulation of fats in the lysosomes destroy the cell.
